Meconium ileus in Cystic Fibrosis

Abstract

Meconium ileus (MI) is often the first manifestation of cystic fibrosis (CF) and occurs in approximately 20% of patients diagnosed with CF. This article reviews the pathophysiology of MI and its clinical presentation. It focuses on the medical and surgical management emphasizing the importance of nutrition and a multidisciplinary approach to improve both short-term and long-term outcomes for CF patients with MI.

Keywords

Cystic fibrosis, Gastrografin, Meconium ileus, Meconium peritonitis

Citation

Sathe, M & Houwen, R 2017, 'Meconium ileus in Cystic Fibrosis', Journal of Cystic Fibrosis, vol. 16 , no. Suppl 2, pp. S32-S39. https://doi.org/10.1016/j.jcf.2017.06.007