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How strict is galactose restriction in adults with galactosaemia? International practice

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Publication date

2015

Authors

Adam, Siddig Momin
Akroyd, R.
Bernabei, S.
Bollhalder, S.
Boocock, S.
Burlina, A.
Coote, T.
Corthouts, K.
Dalmau, Judith
Dawson, S.

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DOI

https://doi.org/10.1016/j.ymgme.2015.03.008

Document Type

Article

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Abstract

Dietary management of 418 adult patients with galactosaemia (from 39 centres/12 countries) was compared. All centres advised lactose restriction, 6 restricted galactose from galactosides. ±. fruits and vegetables and 12 offal. 38% (n. =. 15) relaxed diet by: 1) allowing traces of lactose in manufactured foods (n. =. 13) or 2) giving fruits, vegetables and galactosides (n. =. 2). Only 15% (n. =. 6) calculated dietary galactose. 32% of patients were lost to dietetic follow-up. In adult galactosaemia, there is limited diet relaxation. © 2015 Elsevier Inc..

Keywords

Galactosaemia, Galactose, Lactose, Galactose-1-phosphate, Diet, Monitoring, controlled study, diet restriction, diet therapy, dietary intake, dietetics, dietitian, disease severity, follow up, food processing, fruit, galactose restriction, galactosemia, health survey, human, major clinical study, multicenter study, priority journal, vegetable, clinical trial, comparative study, diet, food, questionnaire, Adult, Food, Fruit, Galactosemias, Humans, Surveys and Questionnaires, Vegetables

Citation

Adam, S M, Akroyd, R, Bernabei, S, Bollhalder, S, Boocock, S, Burlina, A, Coote, T, Corthouts, K, Dalmau, J, Dawson, S, Defourny, S, Meyer, A, Desloovere, A, Devlin, Y, Diels, M, Dokoupil, K, Donald, S, Evans, S, Fasan, I, Ferguson, C, Ford, S, Forga, M, Gallo, G, Grünert, S C, Heddrich-Ellerbrok, M, Heidenborg, C, Jonkers, C F, Lefebure, K, Luyten, K, MacDonald, A, Meyer, U, Micciche, A, Müller, E, Portnoi, P, Ripley, S, Robert, C M, Robertson, L V, Rosenbaum-Fabian, S, Sahm, K, Schultz, E S, Singleton, K, Sjöqvist, E, Stoelen, L, Terry, A, Thompson, S, Timmer, C, Vande Kerckhove, K, van den Ploeg, L, Van Driessche, M, van Rijn, M, van Teeffelen-Heithoff, A, Vitoria, I, Voillot, C, Wenz, J, Westbrook, M, Wildgoose, J & Zweers, H 2015, 'How strict is galactose restriction in adults with galactosaemia? International practice', Molecular Genetics and Metabolism, vol. 115, no. 1, pp. 23-26. https://doi.org/10.1016/j.ymgme.2015.03.008

URI

http://hdl.handle.net/1874/357412