Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy in the Pediatric Population Clinical Characterization and Comparison with Adult-Onset Disease
Publication date
2015-12-01
Authors
te Riele, Anneline S. J. M.
James, Cynthia A.
Sawant, Abhishek C.
Bhonsale, Aditya
Groeneweg, Judith A.
Mast, Thomas P.
Murray, Brittney
Tichnell, Crystal
Dooijes, Dennis
van Tintelen, J. Peter
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Advisors
Supervisors
Document Type
Article
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taverne
Abstract
Objectives The aims of this study were to determine the clinical characteristics and outcomes of pediatric-onset arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) and to compare these with those of adult-onset ARVD/C. Background Improved early detection and increased awareness of ARVD/C have led to a growing group of pediatric patients seeking management recommendations. Prior studies have mainly included adults with ARVD/C; however, clinical features and outcomes may differ in pediatric subjects. Methods Among 502 subjects fulfilling task force criteria for ARVD/C, we identified 75 (15%) with pediatric-onset disease (diagnosis at
Keywords
arrhythmogenic right ventricular dysplasia/cardiomyopathy, children, exercise, outcome, phenotype, Taverne, Cardiology and Cardiovascular Medicine, Physiology (medical)
Citation
Te Riele, A S J M, James, C A, Sawant, A C, Bhonsale, A, Groeneweg, J A, Mast, T P, Murray, B, Tichnell, C, Dooijes, D, Van Tintelen, J P, Judge, D P, van der Heijden, J F, Crosson, J, Hauer, R N W, Calkins, H & Tandri, H 2015, 'Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy in the Pediatric Population Clinical Characterization and Comparison with Adult-Onset Disease', JACC. Clinical electrophysiology, vol. 1, no. 6, pp. 551-560. https://doi.org/10.1016/j.jacep.2015.08.004